Rare disease special product indication comparison table
Indications. |
product |
Phenylketouria |
PHENYL-FREE-I&II (MeadJohnson) PK AID-4 (SHS) Calogen (SHS) Fructose Modjul (SHS) |
1.homocystinuria)2.hypermethioninemia |
HCUAnamix Infant (SHS) Hominex-2 (Abbott) |
maple syrup urine disease |
BCAD(MeadJohnson) |
hereditary tyrosinemia |
Tyrex-1&2 (Abbott) |
urea cycle disorders |
Essential Amino Acid Mix (SHS) Cyclinex-1&2 (Abbott) |
Glutaric aciduria type I |
Glutarex-1&2 (Abbott) GA1 Anamix Infant (SHS) |
3-hydroxy-3-methyl-glutaric acidemia etc. |
I-Valex-2 (Abbott) IVA Anamix Infant (SHS) |
1.propionic acidemia 2.methylmalonic acidemia |
Prominex-1&2 (Abbott) MMA/PA Anamix Infant (SHS) XMTVI Maxamaid (SHS) |
Adrenoleukodystrophy |
Lorenzo’s oil (SHS) |
1.progressive intrahepatic cholestasis 2.inborn errors of bile acid synthesis |
Alfare(Nestle) Generaid Plus (SHS) |
Other Amino Acid Supplements |
L-Arginine (SHS) L-Valine (SHS) L-Leucine (SHS) L-Isoleucine (SHS) Glycine (SHS) |
Energy supplements for patients with metabolic disorders. |
PFD(MeadJohnson)
|
Last Modified: