Disease |
Medication |
---|---|
urea cycle disorder |
Arginine HCL Injection |
Homocystinuria |
Cystadane |
Congenital hyperammonemia caused by abnormal urea metabolism due to citrulline deficiency |
Stimol |
Acute and chronic treatment of secondary carnitine deficiency patients with congenital genetic abnormalities of metabolism |
L-Carnitine |
urea cycle disorder |
Buphenyl |
Tetrahydrobiopterin dificiency |
BH4 |
The hyperinsulinism/hyperammonemia syndrome |
Proglycem (Diazoside) |
Non-Ketotic hyperglycinemia |
Sodium Benzoate |
Porphyria |
Normosang |
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