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罕病營養品

 

 

罕見疾病特品適應症對照表

適用症狀 品項
苯酮尿症(Phenylketouria) PHENYL-FREE-I&II (MeadJohnson)
PK AID-4 (SHS)
Calogen (SHS)
Fructose Modjul (SHS)
1.高胱胺酸尿症(homocystinuria)
2.高甲硫胺酸血症(hypermethioninemia)
HCUAnamix Infant (SHS)
Hominex-2 (Abbott)
楓糖漿尿症(maple syrup urine disease) BCAD(MeadJohnson)
遺傳性高酪胺酸血症(hereditary tyrosinemia)  Tyrex-1&2 (Abbott)
尿素循環代謝障礙(urea cycle disorders) Essential Amino Acid Mix (SHS)
Cyclinex-1&2 (Abbott)
戊二酸血症Type I(Glutaric aciduria type I) Glutarex-1&2 (Abbott)
GA1 Anamix Infant (SHS)
白胺酸代謝異常(3-hydroxy-3-methyl-glutaric acidemia etc.) I-Valex-2 (Abbott)
IVA Anamix Infant (SHS)
1.丙酸血症(propionic academia)
2.甲基丙二酸血症(methylmalonic acidemia)
Prominex-1&2 (Abbott)
MMA/PA Anamix Infant (SHS)
XMTVI Maxamaid (SHS)
腎上腺腦白質失養症(Adrenoleukodystrophy) Lorenzo’s oil (SHS)
1.肝內膽汁滯留症(progressive intrahepatic cholestasis)
2.膽酸合成障礙(inborn errors of bile acid synthesis)
Alfare(Nestle)
Generaid Plus (SHS)
其他胺基酸補充品 L-Arginine (SHS)
L-Valine (SHS)
L-Leucine (SHS)
L-Isoleucine (SHS)
Glycine (SHS)
代謝障礙病患能量補充品 PFD(MeadJohnson)

罕見營養品

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